Multilocular cystic neoplasm of renal cell carcinoma: A rare and incidental finding of Clear Renal cell variant

Prachi and Gaurav Sharma

Multilocular cystic renal neoplasm is a rare subtype of clear cell carcinoma with an incidence of 1-2 % of all clear cell carcinomas. Morphologically, it shows numerous cysts surrounded by fibrous capsules and septae containing clear cells. The aim of this case report is that the diagnosis is possible solely by histopathological and immunohistochemically evaluation, which aids in distinguishing it from other cystic clear cell entities, as imaging is inconclusive pre-operatively. Urologists and radiologists should have an adequate understanding of such an entity. Almost all the cases are amenable to partial nephrectomy irrespective of the size and there is no documentation regarding the recurrence and metastasis, which mandates less stringent follow-up postoperatively compared to clear cell carcinoma.